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KMID : 0816120080110010065
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Korean Journal of Pediatric Gastroenterolology and Nutrition
2008 Volume.11 No. 1 p.65 ~ p.69
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A Case of Alagille Syndrome with Atresia of the Hepatic Duct
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Kim Hyo-Sun
Koh Hong
Chung Ki-Sup
Oh Jung-Tak
Park Young-Nyun
Kim Myung-Joon
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Abstract
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A two-month-old baby had acholic stool, neonatal hyperbilirubinemia and congenital heart disease. Atresia of the hepatic duct was confirmed by open cholangiography, which showed a non-opacified intrahepatic bile duct. Liver biopsy and the Kasai operation were performed. Because the liver biopsy pathology revealed a paucity of intrahepatic bile ducts, the patient was diagnosed with the Alagille syndrome. We report the case of an infant diagnosed with the Alagille syndrome with atresia of the hepatic duct. (Korean J Pediatr Gastroenterol Nutr 2008; 11: 65∼69)
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KEYWORD
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Neonatal cholestasis, Alagille syndrome, Intrahepatic bile duct atresia
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